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PULMONARY FIBROSIS
What is Pulmonary Fibrosis?
Pulmonary Fibrosis is a
generalized term that includes any disease that leads to
scarring of the lung. Some of these diseases are
caused by:-
Environmental exposures such as the scarring associated with asbestosis and
silicosis, hypersensitivity pneumonia
- Certain diseases are associated with pulmonary fibrosis such as
collagen vascular diseases such as lupus (systemic lupus erythematosis),
rheumatoid arthritis, scleroderma, mixed connective tissue disease,
polymyositis/dermatomyositis
- Certain drugs such as amiodarone, nitrofurantoin, methotrexate
- Various diseases such as Sarcoidosis, Histiocytosis X,
Lymphangioleiomyomatosis, etc.
- And a group of diseases that are together known as Idiopathic
Interstitial Pneumonias
The word Idiopathic means
"of unknown origin". These diseases are categorized
into:
-
Idiopathic Usual Interstital Pneumonia
(UIP)
-
Desquamative Interstitial Pneumonia
(DIP)
-
Respiratory bronchiolitis -
Interstitial Lung Disease (RB-ILD)
-
NonSpecific Interstitial Pneumonia (NSIP)
-
Cryptogenic Organizing Pneumonia (COP)(also
known as Bronchiolitis Obliterans Organizing Pneumonia (BOOP)
-
Lymphocytic Interstitial Pneumonia
(LIP)
-
Acute Interstitial Pneumona (AIP)
Therapy
Corticosteroids tend to be the mainstay in
the treatment of many of the interstitial lung diseases. DIP and RB-ILD
are associated with smoking and quitting is vital to the treatment of these
diseases.

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